SERUM COPPER LEVELS IN HOMOZYGOUS B-THALASSAEMIA AND SICKLE CELL DISEASE IN COMPARISON TO SERUM IRON LEVELS AND HEPATIC FUNCTION
Abstract
SERUM COPPER LEVELS, SERUM IRON LEVELS AND FIVE PARAMETERS OF CONTROL OF LIVERFUNCTION, WERE DETERMINED AMONG 20 PATIENTS FROM HOMOZYGOUS B-THALASSAEMIA, NON TREATED WITH DESFERRIOXAMIN 15 PATIENTS FROM HOMOZYGOUS B-THALASSAEMIA, TREATED FOR A LONG TIME WITH DESFERRIOXAMIN, AND 20 PATIENTS FROM DREPANOCYTIC DISEASE. PATIENTS WERE COMPARED TO 15 HETEROZYGOTES OF B-THALASSAEMIA, 15 HETEROZYGOTES OF SICKLE-CELL ANAEMIA AND 133 HEALTHY PERSONS. THE CONCLUSIONS ARE AS FOLLOW. 1. LIVER FUNCTION WAS FOUND NORMAL AMONG HEALTHY PERSONS AND ALL GROUPS OF PATIENTS. 2. SERUM NON LEVELS WERE FOUND IN NORMAL LIMITS AMONG HEALTHYPERSONS, HETEROZYGOTES OF B- THALASSAEMIA AND SICKLE-CELL ANAEMIA, AND IN THE MOST OF HOMOZYGOTES OF B-THALASSAEMIA NON TREATED WITH DESFERRIOXAMIN, BUT HIGH AMONG HOMOZYGOTES OF B-THALASSAEMIA, TREATED FOR A LONG TIME WITH DESFERRIOXAMIN AND PATIENTS FROM DREPANOCYTES DISEASE. 3. SERUM COPPER LEVELS WERE FOUND IN NORMAL LIMITS AMONG HEALTHY PERSONS AND ALL PATI ...
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